Renal anastomotic hemangioma (AH) is a rare, benign vascular tumor with unique histopathological features, a disease that is clinically rare, and existing clinical cases offer different treatment options. As reported in the text, this is a very unusual case of renal AH with AH secondary to residual renal tissue after renal clear cell carcinoma, describing a rare renal AH and a history of renal clear cell carcinoma, including ultrasound, computed tomography and magnetic resonance imaging. However, the available imaging data and the literature do not provide an effective basis for the diagnosis of the disease, raising the lack of understanding and misdiagnosis, where the patient eventually underwent nephrectomy, but the author is not the most appropriate surgical treatment. The postoperative pathological results of the patient are benign lesions, and it is undeniable that nephrectomy is suspected to be overtreated. By reading the literature, we provide different insights into the treatment of the patient, and we hope that this paper can provide some help for the future clinical diagnosis and treatment.