The Hidden Connection - Split Notochord Syndrome with Dorsal Enteric Fistula.

• Tác giả: Suraj Gandhi, Kshitij Mane, Neha Masrani, Ameya Muzumdar, Salmaan Radiowala, Hemanshi Shah, Neha Sisodiya Shenoy, Shravya Subhash Shetty
• Ngôn ngữ: eng
• Ký hiệu phân loại: 363.34987 Other aspects of public safety
• Thông tin xuất bản: India : Journal of Indian Association of Pediatric Surgeons , 2025
• Bộ sưu tập: NCBI
• ID: 212794

Tóm tắt

Split notochord with dorsal enteric fistula is a rare congenital disease of the central nervous system. It can be associated with other anomalies. Communication with gastrointestinal tract is one of them. Less than 30 cases of such dorsal enteric fistula with split notochord have been reported till date. Here, the authors describe a unique case of a female infant with split notochord syndrome and dorsal enteric fistula. A comprehensive assessment is essential to plan management of this infrequent disease. She was treated with a multistage surgical repair and is currently thriving well.