Left ventricular outflow tract obstruction may become apparent after successful aortic valve replacement for severe aortic stenosis, necessitating both aortic valve replacement and septal myectomy. Despite significant advancements in minimally invasive surgery, the current literature on concurrent minimally invasive cardiac procedures is limited due to the varying optimal exposures required for each procedure. In this context, we present a case of aortic valve replacement with concomitant septal myectomy using a minimally invasive, totally endoscopic approach.