Bullous pemphigoid.

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Tác giả: Hossein Akbarialiabad, Adela Rambi G Cardones, Maryam Daneshpazhooh, Dipankar De, Pascal Joly, Yen Loo Lim, Anisa Mosam, Dedee F Murrell, Aikaterini Patsatsi, Enno Schmidt, Kaisa Tasanen, Jun Yamagami

Ngôn ngữ: eng

Ký hiệu phân loại:

Thông tin xuất bản: England : Nature reviews. Disease primers , 2025

Mô tả vật lý:

Bộ sưu tập: NCBI

ID: 232249

Bullous pemphigoid is a chronic, subepidermal autoimmune blistering disease characterized by tense blisters on erythematous or normal skin that predominantly affects the older population. The disease arises from autoantibodies targeting hemidesmosomal proteins BP180 and BP230, which are crucial for dermal-epidermal adhesion. The incidence of bullous pemphigoid is increasing, attributed to an ageing population and improved diagnostic recognition. Genetic predisposition, environmental triggers and associations with other autoimmune disorders underline its multifactorial nature. Diagnosis involves clinical presentation, histopathology, direct immunofluorescence and serological tests. Treatment aims to reduce symptoms and prevent new blister formation, using corticosteroids, immunosuppressive agents and biologics such as rituximab and omalizumab. Despite therapeutic advancements, challenges persist in long-term management, especially in older patients with comorbidities. Ongoing research into molecular mechanisms and novel therapeutic targets and clinical trials are crucial for the development of safer and more effective treatments.
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