U vỏ thượng thận ở trẻ em: báo cáo 29 ca bệnh / U xơ đơn độc dạng mỡ ác tính ở phổi - Tổng quan tài liệu và báo cáo ca bệnh

0 Người đánh giá. Xếp hạng trung bình 0

Tác giả: Phương Thảo Bùi, Thị Bích Ngọc Cấn, Văn Công Cung, Ngọc Thạch Hoàng, Ngọc Khánh Nguyễn, Phú Đạt Nguyễn, Thanh Liêm Nguyễn, Thị Hoàn Nguyễn, Ngọc Sơn Trần, Chí Dũng Vũ

Ngôn ngữ: vie

Ký hiệu phân loại: 610616.994 Medicine and health

Thông tin xuất bản: Y học việt nam, Tạp chí Nghiên cứu y học (Đại học Y Hà Nội), 20122022

Mô tả vật lý: 325-329, 252-263

Bộ sưu tập: Metadata

ID: 482423

Thêm vào giỏ

The adrenal cortex tumors include both malignant adrenal cortex cancers (ACC) and benign masses (ACT) that can be either secreting, of one of the hormones normally produced in the adrenal cortex or non-secretory. Objectives: To describle clinical features and laboratory finding of patients with adrenal cortex tumors. Subjects and methods: This is a case series report. The authors have reviewed in detail the presenting features and laboratory of 29 cases of childhood ACT treated at the Vietnam National Hospital of Pediatrics in a period of 1995-2011. Results: 29 patients, 15 boys and 14 girls. The median age at diagnosis was 4.97 + or - 3.61 years (range, 20 days to 14 years)
19 patients were younger than 5 years. Hypertension and cushingoid features were common in patients (62 percent, 58.6 percent), virilization was presenting feature in 44.8 percent of the group. An abdominal mass was palpable in 20.7 percent of the patients. High level of testosterone was common in patients (94.1 percent). 30 percent of the patients had hypercotisonemia. All tumors were unilateral
the right adrenal glands predominated over left (1.9 :1). 62.5 percent tumors over 4 cm. 22 patients had received operation to remove the tumors: 11 carcinoma, 2 adenocarcinoma. In conclusion: High percentage of patients had malignant tumors among ACC operated patients.U xơ đơn độc (Solitary Fibrous Tumor - SFT) là bệnh hiếm gặp, có thể xảy ra ở nhiều cơ quan trong cơ thể. Bản chất mô bệnh học SFT có nguồn gốc trung mô và có dấu ấn đặc hiệu đối với nhuộm hoá mô miễn dịch. Hai dạng thường gặp là SFT dạng mạch và SFT dạng mỡ. Phần lớn SFT là lành tính song cũng có thể hiện ác tính. Tại ngực, SFT thường thấy xuất hiện ở màng phổi. U xơ đơn độc ở phổi (Solitary Fibrous Tumor of the chest - SFTC) rất hiếm gặp, và u xơ đơn độc dạng mỡ ác tính ở phổi (Malignant Lipomatous Solitary Fibrous Tumor of the chest - MLSFTC) lại càng hiếm gặp hơn. Chúng tôi giới thiệu ca bệnh LSFTC ác tính với mục tiêu phân tích về đặc điểm giải phẫu bệnh và hình ảnh cắt lớp vi tính ngực, mong muốn được bổ sung vào ngân hàng các bệnh hiếm gặp ở phổi, qua đó giúp các bác sỹ sẽ có cách tiếp cận chính xác khi gặp ca bệnh tương tự.

1. Đọc trực tuyến

1. Đọc trực tuyến

Tạo bộ sưu tập với mã QR