Study on 83 cases of congenital cystic denomatoid malformation (CCAM) in children underwent surgical treatment at the National Hospital of Pediatrics from 1 - 2006 to 4 - 2011. The common clinical symptoms were findings of the recu"ent respiratoy infections: chronique cough (81.9 percent), fever (72.3 percent), breathlessness (30.1 percent), reduced breath sounds (84,3 percent), moist rales (50,5 percent). Diagnostic imaging (chest X-ray and CT-scan) presents 100 percent of cases having space-accupying lesions with air and fluid filled-cysts in the diseased lung. Reasons for hospitalization by prenatal diagnosis of CCAM was only 2.4 percent. Surgical intervention was lobectomy of the involved lobe (59 percent by video-assisted thoracic surgery [VATS], 18.1 percent by VATS following by thoracotomy and 22.9 percent by thoracotomy). Early postoperative results: mortality 1.2 percent, air leak of bronchial stump 2.4 percent (repaired by the second thorascopy). The long-term follow up results ( 2 years): good 88.7 percent, moderately good 8.5 percent, moderate 2.8 percent. It came to the conclusion that resection of the involved lobe (lobectomy), especially by VATS was an effective and safe surgical intervention in treatment of CCAM in children.