Low-grade appendiceal mucinous neoplasms (LAMNs) are rare benign tumors of the appendix with possible life-threatening complications. A 25-year-old female patient presented to the emergency room with abdominal pain with symptoms concerning for acute appendicitis. After imaging, it was decided to proceed with an appendectomy. Final pathology showed low-grade appendiceal mucinous neoplasm. Due to their ability to mimic appendicitis, it is important to include LAMNs in the differential diagnosis for patients of all ages, as they can cause life-threatening pseudomyxoma peritonei (PMP). Although this case report highlights a rare condition, it should be on a general surgeon's differential to avoid potential long-term malignancies.