BACKGROUND: Pulmonary arteriovenous fistulas (PAVFs) are abnormal vascular malformations that connect pulmonary arteries and pulmonary veins, resulting in a right-to-left shunt. This anatomical shunt leads to a decrease in arterial oxygen saturation. Patients with PAVFs are usually treated with embolization or surgical procedures. CASE SUMMARY: A 15-month-old child was diagnosed with PAVF DISCUSSION: Here, we report a case of a paediatric patient with congenital asymptomatic PAVF, diagnosed prenatally, and successfully treated with detachable balloon embolization. The case illustrates the detachable occlusion balloons appear to be an effective tool for embolization of PAVF in children, especially in cases involving large feeding vessels.