In this case we report rare clinical entity of Millers syndrome in a small child of 6 years. It is basically an autosomal recessive condition characterized by anomalies of face and limbs such as malar hypoplasia, micrognathia, cleft lip and palate, restricted airway, bones and joints malformations [1, 2]. In this child apart from all these features we came across bleeding nasal masses attached to the inferior tubinates, which were causing complete nasal obstruction. Nasal mass was surgically removed and sent for histopathological examination. It turned out to be nasal polyp with very high vascularity containing mucopolysaccharide material.