German Cohort Observational Study to Investigate the Short- and Long-Term Safety and Clinical Effectiveness of Afamelanotide 16 mg (SCENESSE) in Patients With Erythropoietic Protoporphyria (EPP).

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Tác giả: Pilar Bilbao, Malgorzata Bochno, Daniela Bruch-Gerharz, Bernhard Homey, Regine Keller-Melchior, Lea Kiefer, Kathrin Schelonke, Carla Marie Schlegel, Petra Staubach-Renz, Ulrich Stölzel, Gillian Walker, Joanna Wegner, Karsten Weller

Ngôn ngữ: eng

Ký hiệu phân loại:

Thông tin xuất bản: England : Photodermatology, photoimmunology & photomedicine , 2025

Mô tả vật lý:

Bộ sưu tập: NCBI

ID: 711453

 BACKGROUND: Afamelanotide 16 mg (SCENESSE) is the first approved treatment for erythropoietic protoporphyria (EPP). EPP is a rare autosomal recessive inherited disorder of the haem biosynthesis pathway, where patients experience severe and debilitating acute phototoxicity. It affects at least one in 140,000 of the European population. A postauthorisation safety study (PASS) and a disease registry were imposed as conditions of the European marketing authorisation. OBJECTIVES: Evaluate the short- and long-term safety and clinical effectiveness of afamelanotide 16 mg in EPP patients enrolled in the PASS in Germany. METHODS: The PASS (EUPAS13004) is an ongoing observational study collecting safety and effectiveness variables from treated and untreated EPP patients in the European EPP Disease Registry. Patients (n = 200, none untreated) received afamelanotide according to the summary of product characteristics. Treatment-emergent adverse events were collected as safety variables. Clinical effectiveness was assessed with the EPP-QoL tool and through treatment continuity. RESULTS: The short- and long-term safety and benefit-risk profile of afamelanotide under real-world conditions is consistent with the positive safety profile seen in clinical trials. EPP patients reported a significant increase in QoL compared with baseline values (p <
  0.0001) and 91.0% of patients who started treatment continue being treated. The safety profile of afamelanotide in patients over 70 years of age is consistent with the overall patient population. CONCLUSIONS: Afamelanotide treatment was highly effective and associated with a higher QoL in EPP patients. The study shows a positive safety profile of afamelanotide, with the treatment providing an ongoing clinical benefit.
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